English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 aƱos y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.

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The documents contained in this web site are presented for information enferrmedad only. Dehos Pages ee22 Pages Previous article Next article.

Subscribe to our Newsletter. Management and treatment Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases. Are you a health professional able to prescribe or dispense drugs?

Face, scalp, palms of hands and soles of feet are rarely involved.

Orphanet: Enfermedad de Degos

In the year has been indexed degow the Medlinedatabase, and has become a vehicle for expressing the most current Spanish medicine and modern. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. Health care resources for this disease Expert centres 69 Diagnostic tests 0 Edgos organisations 21 Orphan drug s 0.

From Monday to Friday from 9 a. Over several days, the center of the lesions sinks and develops a characteristic morphology: Show more Show less. Print Send enfermeedad a friend Export reference Mendeley Statistics. MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.

Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed. Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal. CiteScore measures average citations received per document published.


No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested enfemredad in fnfermedad case with intestinal and CNS manifestations. Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described.

enfermedad de degos

Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs. You can change the settings or obtain more information by clicking here. Differential diagnosis The histology of early enfermddad resembles cutaneous lupus erythematosus see this term.

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Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. Check this box if you wish to receive a copy of deegos message. The etiopathogenesis of the disease remains unknown. Si continua navegando, consideramos que acepta su uso.

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A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis. Pemphigus Vegetans in the Inguinal Folds.

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In early stages, histology of lesions may reveal a superficial enfrmedad deep perivascular lymphocytic infiltration with distinct mucin deposition. This condition is chronic and lesions persist over years, often throughout life. Only comments written in English can be processed. Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions.

If you are a member of the AEDV: All articles vegos subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style.


Summary Epidemiology Less than cases have been described in the literature. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis. Many patients have been reported to have defects in blood coagulation.

For all other comments, please send your remarks via contact us. Specialised Social Services Eurordis directory. More developed lesions can imitate lichen sclerosus see this term.

More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis. As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory.

Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. Systemic manifestations are progressive and may lead to serious complications: Go to the members area of the website of the AEDV, https: To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior.

Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.

Additional information Further information on this disease Classification s 3 Gene s 0 Clinical signs and symptoms Publications in PubMed Other website s 7.